Congenital double lip: A report of two cases, one associated with Ascher’s syndrome, highlighting clinical presentation and surgical management of a rare orofacial deformity: Congenital double lip with Ascher’s syndrome

Peter Ngala

doi:10.28982/josam.8335

Authors

Peter Ngala Department of Oral Maxillofacial Surgery, Catholic University of Health and Allied Sciences, Tanzania https://orcid.org/0009-0000-2054-2729

DOI:

https://doi.org/10.28982/josam.8335

Keywords:

Double lip, Cupid's bow shape, Ascher's syndrome, Transverse elliptical excision

Abstract

Double lip is an uncommon oral anomaly characterized by an additional fold of redundant mucosal tissue on the inner aspect of the lip, most frequently affecting the upper lip. It may present as an isolated finding or as part of Ascher’s syndrome, which comprises the triad of double lip, blepharochalasis, and non-toxic thyroid enlargement. This condition primarily causes esthetic and functional concerns, affecting speech and smiling. Diagnosis is clinical, and surgical excision is the standard treatment to restore normal esthetics and function. This report describes two adult male patients with congenital double upper lip, their clinical presentation, and surgical management, which yielded excellent esthetic and functional results. The association of this condition with Ascher’s syndrome is also presented and reviewed.

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References

Khatri A, Kalra N, Tyagi R, Poswal A, Panwar G, Garg K. Double Lip–An Atypical Facial Anomaly: Two Case Reports. Int J Clin Pediatr Dent. 2018;11(5):451-5. doi: 10.5005/jp-journals-10005-1556. DOI: https://doi.org/10.5005/jp-journals-10005-1556

Ismaeley de Andrade T, de Moraes Castanha D, Silva de Andrade J, de Oliveira Sampaio D, de Farias Batista CF. Cheiloplasty in Functional Aesthetic Treatment for Bilateral Double Lip: Case Report. Int J Oral Dent Health. 2019;5:93. doi: 10.23937/2469-5734/1510093.

Srivastava A, Parihar A, Soni R, Shashikanth MC, Chaturvedi TP. Surgical management of a rare case of congenital doubleupper lip. Case Rep Med. 2011;2011:824634. doi: 10.1155/2011/824634. DOI: https://doi.org/10.1155/2011/824634

Desai VD, Das S, Kumar SMV, Sadhwani H. Maxillary double lip: A case series with review of literature. J Indian Acad Oral Med Radiol. 2015;27(2):284-7. doi: 10.4103/0972-1363.170173. DOI: https://doi.org/10.4103/0972-1363.170173

Daniels JSM. Congenital double upper lip: A case report and review of the literature. Saudi Dent J. 2010;22(3):151-3. doi: 10.1016/j.sdentj.2010.04.001. DOI: https://doi.org/10.1016/j.sdentj.2010.04.001

Santos PPDA, Alves PM, Freitas VS, De Souza LB. Double lip surgical correction in Ascher’s syndrome: Diagnosis and treatment of a rare condition. Clinics (Sao Paulo). 2008;63(5):709-12. doi: 10.1590/S1807-59322008000500022. DOI: https://doi.org/10.1590/S1807-59322008000500022

Simão T, Tarazona MJM, Renaux P, Souto R, Azulay L, Fonseca JCM. Ascher syndrome: Diagnosis and surgical approach. Surg Cosmet Dermatol. 2015;7(3):268-71. doi: 10.5935/scd1984-8773.201573433. DOI: https://doi.org/10.5935/scd1984-8773.201573433

Palma MC, Taub DI. Recurrent double lip: literature review and report of a case. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2009;107(3):e20-3. doi: 10.1016/j.tripleo.2008.11.016. DOI: https://doi.org/10.1016/j.tripleo.2008.11.016

Aggarwal T, Chawla K, Lamba AK, Faraz F, Tandon S. Congenital Double Lip: A Rare Deformity Treated Surgically. World J Plast Surg. 2014;3(1):74-7.

Srivastava A, Chaudhri S, Yadav AK, Srivastava S. Management of double lip. J Clin Diagn Res. 2017;11(8):ZD27-9. doi: 10.7860/JCDR/2017/28816.10492. DOI: https://doi.org/10.7860/JCDR/2017/28816.10492

Siwach A, Mittal R, Mattoo KA, Goswami R. Congenital Double Lip with Cleft Palate and Bifid Uvula: A Rare Case Report. Univ J Dent Sci. 2019;5(1):47-9.

Zardawi FM, Gul SS, Hama BJ, Khursheed DA. Double Lip: A Review of Literature and a Case Report. Sulaimani Dent J. 2018;5(2):142-7. doi: 10.17656/sdj.10082. DOI: https://doi.org/10.17656/sdj.10082

Donato CMG, Santos Netto JDN, Melo DF. Do you know this syndrome? Ascher´s syndrome: Clinical findings of little known triad. An Bras Dermatol. 2017;92(5):729-30. doi: 10.1590/abd1806-4841.20177158. DOI: https://doi.org/10.1590/abd1806-4841.20177158

Ramesh BA. Ascher syndrome: Review of literature and case report. Indian J Plast Surg. 2011;44(1):147-9. doi: 10.4103/0970-0358.81468. DOI: https://doi.org/10.4103/0970-0358.81468

Lewandowski B, Brzęcka D, Brodowski R. Surgical management of double lip: A case report. Eur J Paediatr Dent. 2020;21(3):197-8. doi: 10.23804/ejpd.2020.21.03.07.

Gupta V, Khandpur S. Blepharochalasis with double lip: A case of Ascher syndrome. Indian J Dermatol Venereol Leprol. 2015;81(6):621-2. doi: 10.4103/0378-6323.158645. DOI: https://doi.org/10.4103/0378-6323.158645

Zhao ZL, Wang SM, Shao CY, Fu Y. Ascher syndrome: A rare case of blepharochalasis combined with double lip and hashimoto’s thyroiditis. Int J Ophthalmol. 2019;12(6):1028-30. doi: 10.18240/ijo.2019.06.26. DOI: https://doi.org/10.18240/ijo.2019.06.26

Al-Hassani M, Carey B, Sanderson J, Hullah E, Escudier M. Ascher’s syndrome: A rare cause of lip swelling. Ann R Coll Surg Engl. 2020;102(8):e216-8. doi: 10.1308/RCSANN.2020.0161. DOI: https://doi.org/10.1308/rcsann.2020.0161

Kandamani J, Gouthaman SS, Ramakrishnan DS, Santhosh Kumar MP. Surgical correction of congenital double lip-a case report. Int J Res Pharm Sci. 2020;11(4):6004-7. doi: 10.26452/ijrps.v11i4.3263. DOI: https://doi.org/10.26452/ijrps.v11i4.3263

Pasqual GF, Sá LDV, Tissiani LAL. Bilabial double lip. Rev Bras Cir Plást. 2015;30(2):345-8. doi: 10.5935/2177-1235.2015rbcp0151. DOI: https://doi.org/10.5935/2177-1235.2015RBCP0151

De Figueredo AA, De Pochat VD, Barreto TF, Mendes RS, Alonso N, Meneses JV. Management of an unusual presentation of ascher syndrome. J Craniofac Surg. 2012;23(6):e589-91. doi: 10.1097/SCS.0b013e31825dabec. DOI: https://doi.org/10.1097/SCS.0b013e31825dabec