Pigmented villonodular synovitis of the knee confused with juvenile rheumatoid arthritis in a 3-year-old child: A case report

Ertuğrul Şahin; Hasan Tatari

doi:10.28982/josam.716164

Authors

Ertuğrul Şahin https://orcid.org/0000-0002-8509-3570
Hasan Tatari https://orcid.org/0000-0002-7661-9606

DOI:

https://doi.org/10.28982/josam.716164

Keywords:

PVNS, Pediatric, Knee, Juvenile Rheumatoid Arthritis

Abstract

Pigmented villonodular synovitis (PVNS) is rare and characterized by diffuse synovial cell proliferation with the development of villi, or round/ovoid lobulated nodules of varied sizes. It usually presents in adults between the ages of 30 and 40 years and is uncommon in the pediatric population. We herein report a 3-year-old female patient with PVNS causing a femoral subchondral lesion in the right knee. Her symptoms started at the age of one and she had gotten treatment for juvenile rheumatoid arthritis for 2 years. The patient was operated, and the tumor was excised. Arthrotomy was performed for diffuse PVNS and diagnosis was made histopathologically. She was followed-up for 18 months with clinical examinations and MRI, as necessary. She had no pain or limitation in range of motion. She is currently fully functional and ambulatory.

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