Year 2020, Volume 4 , Issue 1, Pages 93 - 95 2020-01-02

Akut peritonit sırasında tesadüfen fark edilen konjenital izole asplenia
Congenital isolated asplenia accidentally discovered during acute peritonitis

Elmarouni ABDELOUHAB [1] , Karam AZIZ [2] , Et-tayeb OUZZANI [3] , Ahmed ZERHOUNI [4] , Tarik SOUIKI [5] , Karim IBN MAJDOUB EL HASSANI [6] , Khalid MAZAZ [7] , Imane TOUGHRAI [8]


Çok nadir görülen bir durum olan konjenital aspleninin 2 farklı tipi vardır: heterotaksi sendromları ve izole konjenital aspleni (ICA). Ivemark sendromu, asplenia, kalbin malformasyonları ve göğüs ve karındaki iç organların malpozisyonu ile karakterize heterotaksi sendromlarından biridir. ICA vakaları çocuklukta da ölümcüldür, ancak bildirilen canlı yetişkin vakaları mevcuttur. Etkilenenler tipik olarak fulminan sepsis için yüksek risk altındadır ve trombositoz ve mezenterik tromboz gibi bulaşıcı olmayan komplikasyon riski daha yüksektir. Burada ülser perforasyonuna bağlı peritonit için acil bir laparotomi sırasında tesadüfen saptanan doğuştan asplenisi olan bir hastanın olağandışı olgusunu sunuyoruz.

An extremely rare condition, congenital asplenia has 2 distinct types: heterotaxy syndromes and isolated congenital asplenia (ICA). Ivemark syndrome is one of the heterotaxy syndromes characterized by asplenia, malformations of the heart, and malposition of internal organs in the chest and abdomen. ICA cases are also fatal in childhood, but there are reported living adult cases. Those affected are typically at increased risk for fulminant sepsis and carry a higher risk of noninfectious complications, such as thrombocytosis and mesenteric thrombosis. We herein report the unusual case of a patient with congenital asplenia, which was discovered fortuitously during an emergency laparotomy for peritonitis due to ulcer perforation.

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Primary Language en
Subjects Surgery
Journal Section Case report
Authors

Orcid: 0000-0003-2035-7982
Author: Elmarouni ABDELOUHAB (Primary Author)
Institution: visceral surgery service, Hassan II university hospital, faculty of medicine and pharmacy of fez, sidi Mohamed Ben Abdullah university, fez ,Morocco
Country: Morocco


Orcid: 0000-0002-3330-7311
Author: Karam AZIZ
Institution: visceral surgery service, Hassan II university hospital, faculty of medicine and pharmacy of fez, sidi Mohamed Ben Abdullah university, fez ,Morocco
Country: Morocco


Orcid: 0000-0003-2977-2904
Author: Et-tayeb OUZZANI
Institution: visceral surgery service, Hassan II university hospital, faculty of medicine and pharmacy of fez, sidi Mohamed Ben Abdullah university, fez , Morocco
Country: Morocco


Orcid: 0000-0001-8441-016X
Author: Ahmed ZERHOUNI
Institution: Visceral Surgery Service, Hassan II University Hospital, Faculty of Medicine and Pharmacy of Fez, Sidi Mohamed Ben Abdullah University, Fez, Morocco
Country: Morocco


Orcid: 0000-0001-5657-7253
Author: Tarik SOUIKI
Institution: visceral surgery service, Hassan II university hospital, faculty of medicine and pharmacy of fez, sidi Mohamed Ben Abdullah university, fez ,Morocco
Country: Morocco


Orcid: 0000-0002-0421-7296
Author: Karim IBN MAJDOUB EL HASSANI
Institution: visceral surgery service, Hassan II university hospital, faculty of medicine and pharmacy of fez, sidi Mohamed Ben Abdullah university, fez ,Morocco
Country: Morocco


Orcid: 0000-0001-7779-7802
Author: Khalid MAZAZ
Institution: visceral surgery service, Hassan II university hospital, faculty of medicine and pharmacy of fez, sidi Mohamed Ben Abdullah university, fez ,Morocco
Country: Morocco


Orcid: 0000-0003-0401-3012
Author: Imane TOUGHRAI
Institution: visceral surgery service, Hassan II university hospital, faculty of medicine and pharmacy of fez, sidi Mohamed Ben Abdullah university, fez ,Morocco
Country: Morocco


Dates

Publication Date : January 2, 2020

Bibtex @case report { josam588198, journal = {Journal of Surgery and Medicine}, issn = {}, eissn = {2602-2079}, address = {jsurgmed@gmail.com}, publisher = {Fatih BAŞAK}, year = {2020}, volume = {4}, pages = {93 - 95}, doi = {10.28982/josam.588198}, title = {Congenital isolated asplenia accidentally discovered during acute peritonitis}, key = {cite}, author = {Abdelouhab, Elmarouni and Azız, Karam and Ouzzanı, Et-tayeb and Zerhounı, Ahmed and Souıkı, Tarik and Ibn Majdoub El Hassanı, Karim and Mazaz, Khalid and Toughraı, Imane} }
APA Abdelouhab, E , Azız, K , Ouzzanı, E , Zerhounı, A , Souıkı, T , Ibn Majdoub El Hassanı, K , Mazaz, K , Toughraı, I . (2020). Congenital isolated asplenia accidentally discovered during acute peritonitis . Journal of Surgery and Medicine , 4 (1) , 93-95 . DOI: 10.28982/josam.588198
MLA Abdelouhab, E , Azız, K , Ouzzanı, E , Zerhounı, A , Souıkı, T , Ibn Majdoub El Hassanı, K , Mazaz, K , Toughraı, I . "Congenital isolated asplenia accidentally discovered during acute peritonitis" . Journal of Surgery and Medicine 4 (2020 ): 93-95 <http://jsurgmed.com/en/pub/issue/51597/588198>
Chicago Abdelouhab, E , Azız, K , Ouzzanı, E , Zerhounı, A , Souıkı, T , Ibn Majdoub El Hassanı, K , Mazaz, K , Toughraı, I . "Congenital isolated asplenia accidentally discovered during acute peritonitis". Journal of Surgery and Medicine 4 (2020 ): 93-95
RIS TY - JOUR T1 - Congenital isolated asplenia accidentally discovered during acute peritonitis AU - Elmarouni Abdelouhab , Karam Azız , Et-tayeb Ouzzanı , Ahmed Zerhounı , Tarik Souıkı , Karim Ibn Majdoub El Hassanı , Khalid Mazaz , Imane Toughraı Y1 - 2020 PY - 2020 N1 - doi: 10.28982/josam.588198 DO - 10.28982/josam.588198 T2 - Journal of Surgery and Medicine JF - Journal JO - JOR SP - 93 EP - 95 VL - 4 IS - 1 SN - -2602-2079 M3 - doi: 10.28982/josam.588198 UR - https://doi.org/10.28982/josam.588198 Y2 - 2020 ER -
EndNote %0 Journal of Surgery and Medicine Congenital isolated asplenia accidentally discovered during acute peritonitis %A Elmarouni Abdelouhab , Karam Azız , Et-tayeb Ouzzanı , Ahmed Zerhounı , Tarik Souıkı , Karim Ibn Majdoub El Hassanı , Khalid Mazaz , Imane Toughraı %T Congenital isolated asplenia accidentally discovered during acute peritonitis %D 2020 %J Journal of Surgery and Medicine %P -2602-2079 %V 4 %N 1 %R doi: 10.28982/josam.588198 %U 10.28982/josam.588198
ISNAD Abdelouhab, Elmarouni , Azız, Karam , Ouzzanı, Et-tayeb , Zerhounı, Ahmed , Souıkı, Tarik , Ibn Majdoub El Hassanı, Karim , Mazaz, Khalid , Toughraı, Imane . "Congenital isolated asplenia accidentally discovered during acute peritonitis". Journal of Surgery and Medicine 4 / 1 (January 2020): 93-95 . https://doi.org/10.28982/josam.588198
AMA Abdelouhab E , Azız K , Ouzzanı E , Zerhounı A , Souıkı T , Ibn Majdoub El Hassanı K , Mazaz K , Toughraı I . Congenital isolated asplenia accidentally discovered during acute peritonitis. J Surg Med. 2020; 4(1): 93-95.
Vancouver Abdelouhab E , Azız K , Ouzzanı E , Zerhounı A , Souıkı T , Ibn Majdoub El Hassanı K , Mazaz K , Toughraı I . Congenital isolated asplenia accidentally discovered during acute peritonitis. Journal of Surgery and Medicine. 2020; 4(1): 93-95.