Polispleni / heterotaksi sendromu, torasik ve abdominal organların yanlış dağılımı sonucu olarak ortaya çıkan çok nadir görülen bir durumdur. Farklı klinik özelliklere ve anatomik varyasyonlara sahip iki grupta incelenmiştir; sağ ve sol izomerizm. Sağ yan ağrısı ve böbrek taşı şüphesi nedeniyle kontrastsız bilgisayarlı tomografi (BT) çekimi yapılan 47 yaşındaki kadın hastada, sol izomerizm – polispleni sendromu ve eşlik eden abdominal organ varyasyonları saptandı. Abdominal BT incelemesinde sağ üst kadranda yerleşimli mide ve çok sayıda dalak, orta hat yerleşimli karaciğer tespit edildi. İnferior vena kava devamlılığında kesilme ve azigos devamlılığı tespit edildi. Hepatik venler doğrudan sağ atriyuma drene oluyordu. Tespit edilen bulgular, polispleni-sol izomerizm ile uyumlu olarak değerlendirildi. Retroaortik sol renal ven, çekum malpozisyonu ve dorsal pankreas agenezisine izomerizm eşlik ediyordu. Literatürde ayrı ayrı rapor edilen sol izomerizme eşlike eden retroaortik sol renal ven ve dorsal pankreas agenezisi olgu sunumları mevcuttu. Ancak bu üç anomalinin eşlik ettiği olgu sunumu yoktu ve bu özellikleriyle olgumuz tekdi. Anatomik varyasyonları ve klinik durumu bilmek yanlış tanıyı önleyebilir ve olası bir cerrahi işlemin planlanmasında görüntüleme bulgularını bilmek çok önemlidir.
Polysplenia / heterotaxy syndrome is a very rare condition that occurs as a result of the maldistribution of the thoracic and abdominal organs. It is examined in two groups with different clinical features and anatomical variations: right and left isomerism. This paper reports the case of a 47-year-old female patient who underwent a non-contrast computed tomography (CT) examination due to right flank pain and suspicion of a renal stone and presented with the findings of left isomerism; i.e., accompanied by intraabdominal variations. On abdominal CT examination, stomach and multiple spleen were localized in the right upper quadrant, and the liver had a midline localization. The interruption of the inferior vena cava with azygos continuation were also detected. The hepatic veins were draining directly into the right atrium. In the literature, a retroaortic left renal vein and dorsal pancreatic agenesis have been individually reported to coexist with left isomerism, but no other case of the coincidence of these three anomalies has been described, which makes the current case report significant. Having knowledge of anatomical variations and clinical status can prevent misdiagnosis, and imaging findings are crucial in the planning of a possible surgical procedure.
| Primary Language | en |
|---|---|
| Subjects | Radiology, Nuclear Medicine, Medical Imaging |
| Journal Section | Case report |
| Authors |
|
| Dates |
Publication Date : November 1, 2019 |
| Bibtex | @case report { josam573375,
journal = {Journal of Surgery and Medicine},
issn = {},
eissn = {2602-2079},
address = {jsurgmed@gmail.com},
publisher = {Fatih BAŞAK},
year = {2019},
volume = {3},
pages = {812 - 814},
doi = {10.28982/josam.573375},
title = {Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report},
key = {cite},
author = {Emekli̇, Emre and Gündoğdu, Elif and Kebapçı, Mahmut}
} |
| APA | Emekli̇, E , Gündoğdu, E , Kebapçı, M . (2019). Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report . Journal of Surgery and Medicine , 3 (11) , 812-814 . DOI: 10.28982/josam.573375 |
| MLA | Emekli̇, E , Gündoğdu, E , Kebapçı, M . "Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report" . Journal of Surgery and Medicine 3 (2019 ): 812-814 <http://jsurgmed.com/en/pub/issue/49829/573375> |
| Chicago | Emekli̇, E , Gündoğdu, E , Kebapçı, M . "Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report". Journal of Surgery and Medicine 3 (2019 ): 812-814 |
| RIS | TY - JOUR T1 - Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report AU - Emre Emekli̇ , Elif Gündoğdu , Mahmut Kebapçı Y1 - 2019 PY - 2019 N1 - doi: 10.28982/josam.573375 DO - 10.28982/josam.573375 T2 - Journal of Surgery and Medicine JF - Journal JO - JOR SP - 812 EP - 814 VL - 3 IS - 11 SN - -2602-2079 M3 - doi: 10.28982/josam.573375 UR - https://doi.org/10.28982/josam.573375 Y2 - 2019 ER - |
| EndNote | %0 Journal of Surgery and Medicine Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report %A Emre Emekli̇ , Elif Gündoğdu , Mahmut Kebapçı %T Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report %D 2019 %J Journal of Surgery and Medicine %P -2602-2079 %V 3 %N 11 %R doi: 10.28982/josam.573375 %U 10.28982/josam.573375 |
| ISNAD | Emekli̇, Emre , Gündoğdu, Elif , Kebapçı, Mahmut . "Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report". Journal of Surgery and Medicine 3 / 11 (November 2019): 812-814 . https://doi.org/10.28982/josam.573375 |
| AMA | Emekli̇ E , Gündoğdu E , Kebapçı M . Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report. J Surg Med. 2019; 3(11): 812-814. |
| Vancouver | Emekli̇ E , Gündoğdu E , Kebapçı M . Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report. Journal of Surgery and Medicine. 2019; 3(11): 812-814. |
| IEEE | E. Emekli̇ , E. Gündoğdu and M. Kebapçı , "Coincidence of left isomerism, malposition of cecum, dorsal pancreatic agenesis, and retroaortic left renal vein: A case report", Journal of Surgery and Medicine, vol. 3, no. 11, pp. 812-814, Nov. 2019, doi:10.28982/josam.573375 |