Undifferentiated pleomorphic sarcoma with focal myogenic differentiation mimicking left atrial myxoma

İlke Evrim Seçinti; Didar Gürsoy; Metin Onur Beyaz; İyad Fansa

doi:10.28982/josam.992197

Authors

İlke Evrim Seçinti https://orcid.org/0000-0002-8614-3971
Didar Gürsoy Hatay Mustafa Kemal University, Faculty of Medicine, Department of Pathology https://orcid.org/0000-0002-0674-7047
Metin Onur Beyaz Hatay Mustafa Kemal University, Faculty of Medicine, Department of Cardiovascular Surgery https://orcid.org/0000-0001-9338-8152
İyad Fansa Hatay Mustafa Kemal University, Faculty of Medicine, Department of Cardiovascular Surgery https://orcid.org/0000-0002-5390-5511

DOI:

https://doi.org/10.28982/josam.992197

Keywords:

Left atrium, Myogenic differentiation, Myxoma, Sarcoma

Abstract

Primary cardiac tumors are very rare. Cardiac sarcomas can be detected at any age, regardless of gender. At diagnosis, these are mostly symptomatic and one-third metastatic. Undifferentiated pleomorphic sarcomas account for 1.7% of all cardiac tumors, are typically localized in the left atrium, and involve the mitral valve. Here we present a case of left atrial undifferentiated pleomorphic sarcoma with myogenic differentiation that clinically and radiologically mimicked myxoma.

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References

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