A rare manifestation of Ewing sarcoma: Primary intracranial Ewing sarcoma: Primary intracranial Ewing sarcoma

Eren Kıymaz; Ünal  Özüm

doi:10.28982/josam.8084

Authors

Eren Kıymaz Department of Neurosurgery, Sivas Cumhuriyet University Faculty of Medicine, Sivas, Turkey https://orcid.org/0000-0002-4868-6297
Ünal Özüm Department of Neurosurgery Sivas Cumhuriyet University Faculty of Medicine, Sivas, Turkey https://orcid.org/0000-0003-2065-2033

DOI:

https://doi.org/10.28982/josam.8084

Keywords:

Ewing sarcoma, primary intracranial Ewing sarcoma, dura invasion, muscle invasion, bone invasion

Abstract

Primary intracranial Ewing sarcoma (ES) is an extremely rare condition, frequently presenting as supratentorial and intraparenchymal. This case report presents a 22-year-old male diagnosed with primary intracranial ES exhibiting dura, muscle, and bone invasion. The patient initially presented with swelling in the preauricular region and was operated on with a preliminary diagnosis of meningioma, but pathology confirmed primary intracranial ES. This case highlights the rarity of primary intracranial ES and provides significant contributions to the diagnostic process.

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