Truncus arteriosus with meandering pulmonary arteries: Atypical truncus arteriosus

Emre  Oteyaka; Okan Eren  Kuguoglu; Gizem  Sari; Mehmet Turan  Basunlu; Yilmaz  Yozgat; Murat  Ugurlucan; Halil  Turkoglu

doi:10.28982/josam.1104984

Authors

Emre Oteyaka Istanbul Medipol University Faculty of Medicine, Department of Cardiovascular Surgery, Istanbul, Turkey https://orcid.org/0000-0001-5889-2257
Okan Eren Kuguoglu Istanbul Medipol University Faculty of Medicine, Department of Cardiovascular Surgery, Istanbul, Turkey https://orcid.org/0000-0001-7575-5297
Gizem Sari Istanbul Medipol University Faculty of Medicine, Department of Pediatric Cardiology, Istanbul, Turkey https://orcid.org/0000-0001-6602-5946
Mehmet Turan Basunlu Istanbul Medipol University Faculty of Medicine, Department of Pediatric Cardiology, Istanbul, Turkey https://orcid.org/0000-0001-9191-952X
Yilmaz Yozgat Istanbul Medipol University Faculty of Medicine, Department of Pediatric Cardiology, Istanbul, Turkey https://orcid.org/0000-0001-5164-8534
Murat Ugurlucan Biruni University Faculty of Medicine, Department of Cardiovascular Surgery, Istanbul, Turkey https://orcid.org/0000-0001-6643-9364
Halil Turkoglu Istanbul Medipol University Faculty of Medicine, Department of Cardiovascular Surgery, Istanbul, Turkey https://orcid.org/0000-0003-4856-0974

DOI:

https://doi.org/10.28982/josam.1104984

Keywords:

truncus arteriosus, pulmonary artery, classification, surgical treatment

Abstract

Truncus arteriosus is a rare, cyanotic, and congenital heart defect occurring due to failure in the differentiation of the aorta and the pulmonary artery during fetal development. The disease is categorized into four sub-categories in the Van Praagh and Collett & Edwards classification systems according to the origin of the pulmonary arteries. Surgical correction of the pulmonary arteries and repair of the ventricular septal defect is the preferred treatment strategy of choice; this intervention is required early in life. Here, we report a four-month-old baby with truncus arteriosus consisting of atypical pulmonary anatomy undefined by either the Van Praagh or the Collett & Edwards classification systems who underwent successful corrective surgery.

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