Use of video-laryngoscopy in pediatric patients with Ehlers-Danlos syndrome: Two case reports

Mehmet Kenan Erol; Firdevs Kaya

doi:10.28982/josam.551029

Authors

Mehmet Kenan Erol https://orcid.org/0000-0003-1493-8828
Firdevs Kaya https://orcid.org/0000-0002-7512-6340

DOI:

https://doi.org/10.28982/josam.551029

Keywords:

Ehlers-Danlos, Anesthesia, Difficult airway, Video-laryngoscopy

Abstract

Difficult airway management is one of the most challenging situations for an anesthesiologist. If not handled properly, it can lead to severe complications, even death. Video-laryngoscopy (VL) is one of the many techniques developed for this purpose. Ehlers-Danlos Syndrome (EDS) is a rare disease requiring possible difficult airway management due to temporo-mandibular dysfunction or occipito-atlanto-axial instability. We herein present two pediatric EDS cases who required surgery. The first case was a 9-year-old, male, ASA II EDS patient scheduled for strabismus surgery, and the second case was a 12-year-old, male, ASA III EDS patient who was also diagnosed with a brain cyst and lymphoma, due for emergency surgery for acute abdomen. With their heads in a neutral position, both patients were intubated without tissue trauma at first attempt using video-laryngoscopy. No complications were encountered in both cases. We believe that using video-laryngoscopy for managing difficult pediatric airways may be beneficial in avoiding complications.

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