Malignant retroperitoneal paraganglioma treated with radiotherapy: A case report

Sanae Ghammad; Ghita Chebihi Hassani; Fadwa Allouche; Zineb Alami; Touria Bouhafa; Khalid Hassouni

doi:10.28982/josam.456705

Authors

Sanae Ghammad https://orcid.org/0000-0002-7940-8396
Ghita Chebihi Hassani https://orcid.org/0000-0003-2714-1957
Fadwa Allouche https://orcid.org/0000-0002-6793-4911
Zineb Alami https://orcid.org/0000-0003-3349-1793
Touria Bouhafa https://orcid.org/0000-0002-6793-4911
Khalid Hassouni https://orcid.org/0000-0002-1442-255X

DOI:

https://doi.org/10.28982/josam.456705

Keywords:

Retroperitoneal paraganglioma, Radiotherapy, Secretory tumor, Pheochromocytoma

Abstract

Paragangliomas are rare tumors arising from undifferentiated cells of the primitive neural crest. We report a case of a 33-year-old female patient who presented a large firm retroperitoneal tumor situated on the left flank above the left kidney. Levels of the serum epinephrine and norepinephrine were high. We performed a scanned biopsy; the histopathological examination and the immunohistochemical analyses concluded the diagnosis of a retroperitoneal paraganglioma. The tumor was judged secreting and inoperable; therefore it was decided to be treated with radiotherapy.

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